منابع مشابه
Considerations for Fontan Individualization in Patients with Isomerism (Heterotaxy)
Fontan palliation has been used as the final stage in functionally univentricular palpation for several years. The Fontan has undergone several iterations, having begun as an atriopulmonary connection and then evolving into the extracardiac conduit. Innovations in computer modeling and flow simulation has now allowed for studies to be conducted to characterize flow within the Fontan conduit and...
متن کاملAntenatal diagnosis of left atrial isomerism and heterotaxy syndrome in fetus with Meckel-Gruber syndrome.
We aimed to present a fetus with Meckel-Gruber syndrome (MKS) who had left atrial isomerism, heterotaxy syndrome and complete heart block. A 26-year-old healthy female was referred to our clinic in the 23rd week of her pregnancy. The fetus had multiple systemic anomalies including fetal heart. Fetal echocardiography revealed a horizontal liver, left-sided stomach and vena cava interruption with...
متن کاملIsomerism in the setting of the so-called “heterotaxy”: The usefulness of computed tomographic analysis
The most complex combinations of congenital cardiac malformations are found in the setting of bodily isomerism. The question remains, however, as to whether evidence of cardiac isomerism is always to be found in the setting of bodily isomerism, also known as "heterotaxy." We have previously shown that, when assessed on the basis of the extent of the pectinate muscles relative to the atrioventri...
متن کاملImpact of Era, Type of Isomerism, and Ventricular Morphology on Survival in Heterotaxy: Implications for Therapeutic Management.
BACKGROUND Heterotaxy has been demonstrated to reduce survival. There are several different subgroups of patients, however, and no single study has had a large number of patients and analyzed survival across the different subgroups such as patients born in different eras, patients with right and left isomerism, and patients with biventricular or functionally univentricular hearts. This study po...
متن کاملFetal Heterotaxy with Tricuspid Atresia, Pulmonary Atresia, and Isomerism of the Right Atrial Appendages at 22 Weeks
We report the accurate prenatal diagnosis at 22 weeks gestation of right atrial isomerism in association with tricuspid atresia. Several distinctive sonographic features of isomerism of the right atrial appendages were present in this fetus: complex cardiac abnormality, ventriculoarterial discordance, juxtaposition of the aorta and the inferior vena cava to the right side, pulmonary atresia, an...
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ژورنال
عنوان ژورنال: Cardiology in the Young
سال: 2012
ISSN: 1047-9511,1467-1107
DOI: 10.1017/s1047951112000893